Coexistence of Autosomal Dominant Polycystic Kidney Disease and Amyloidosis in a Patient With Nephrotic-range Proteinuria

Authors

  • Ezgi Coskun Yenigun Department of Nephrology, Ankara Numune Research and Education Hospital, Ankara, Turkey
  • Fatih Dede Department of Nephrology, Ankara Numune Research and Education Hospital, Ankara, Turkey
  • Nihal Ozkayar Department of Nephrology, Ankara Numune Research and Education Hospital, Ankara, Turkey
  • Didem Turgut Department of Nephrology, Ankara Numune Research and Education Hospital, Ankara, Turkey
  • Serhan Vahit Piskinpasa Department of Nephrology, Ankara Numune Research and Education Hospital, Ankara, Turkey
  • Ramazan Ozturk Department of Nephrology, Ankara Numune Research and Education Hospital, Ankara, Turkey
  • Eyup Koc Department of Nephrology, Ankara Numune Research and Education Hospital, Ankara, Turkey
  • Ali Riza Odabas Department of Nephrology, Ankara Numune Research and Education Hospital, Ankara, Turkey

Abstract

Autosomal dominant polycystic kidney disease (ADPKD) is an inherited disorder characterized by the development and growth of cysts in the kidneys. Non-nephritic-range proteinuria is a common presentation in ADPKD patients; however, nephrotic syndrome is a rare coincidence. A 52-year-old man is described who was diagnosed with secondary amyloidosis with ADPKD. To our knowledge, this is the first case of amyloidosis associated with frequently infected renal cysts. Patients with ADPKD who show massive proteinuria should be investigated in terms of concomitant glomerular disease.

Downloads

Published

2014-05-28

Issue

Section

CASE REPORT | Kidney Diseases