Kartagener Syndrome With Focal Segmental Glomerulosclerosis

Authors

  • Ali Momeni Division of Nephrology, Department of Internal Medicine, Shahrekord University of Medical Sciences. Shahrekord, Iran Author
  • Behzad Doroushi Division of Rheumatology, Department of Internal Medicine, Shahrekord University of Medical Sciences. Shahrekord, Iran Author
  • Diana Taheri Department of Pathology, Isfahan University of Medical Sciences, Isfahan, Iran Author

Abstract

Primary ciliary dyskinesia is characterized by congenital impairment of mucociliary clearance. Kartagener syndrome (KS) is a clinical variant of primary ciliary dyskinesia which is involved in situs inversus associated with chronic respiratory infections. In addition, glomerular disease in KS syndrome is rare and reported cases are limited. We had a 27-year-old female patient with KS who presented with proteinuria, hematuria, normal kidney function, and a family history of systemic lupus erythematosus. Kidney biopsy showed segmental scar with adhesion to Bowman capsule, which was indicative of focal segmental glomerulosclerosis.

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Author Biography

  • Ali Momeni, Division of Nephrology, Department of Internal Medicine, Shahrekord University of Medical Sciences. Shahrekord, Iran
    internal medicine department shahrekord medical science iran

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Published

2013-11-13

Issue

Section

CASE REPORT | Kidney Diseases

How to Cite

Kartagener Syndrome With Focal Segmental Glomerulosclerosis. (2013). Iranian Journal of Kidney Diseases, 7(6), 499-501. https://www.ijkd.org/index.php/ijkd/article/view/947